====== Sensorineural Hearing Loss ======
  * Ocular screening is recommended due to the frequent co-incidence of ocular disease 
  * Eye exam when first diagnosed and follow up as required. 
 
====Ocular/Visual Screening Recommendations====
  * Complete Eye Exam
  * Additional specialized testing based on findings

==== Ocular Associations ====
  * Anterior Segment Disease
    * Keratitis-ichthyosis-deafness syndrome
  * Posterior Segment Disease
    * [[usher_syndrome|Usher Syndrome]] 
    * Heriditary Optic Neuropathies
      * [[leber_hereditary_optic_neuropathy|Leber Hereditary Optic Neuropathy]]
      * [[bilateral_optic_atrophy|Optic Atrophy]]
      * Wolfram Syndrome
    * Norrie Disease
    * [[stickler_syndrome|Stickler Syndrome]]
    * [[marfan_syndrome|Marfan Syndrome]]
    * Heimler Syndrome
  * Anterior and Posterior Segment Disease
    * Cogan Syndrome
    * Congenital Rubella
    * Alport Syndrome
    * [[waardenburg_syndrome|Waardenburg Syndrome]]


====== Resources ======
  * [[https://1drv.ms/b/c/31d83ae8e55e0542/ESYcuOQ1dwRAtzvkcEzfeA8BFnefBf2dEaiLDS9jDgOVhw?e=SuwITi |Zaheer HA et al. Ocular Manifestations in Patients with Sensorineural Hearing Loss. J Ophthalmic Vis Res 2022:17(4):551-573]]
  * [[https://1drv.ms/b/c/31d83ae8e55e0542/EYCiwix3O6xOkBj0H_RHi98B76GzajoZYj4pa2X7p9hw_w?e=eoCRgd |Principles and Guidelines for Early Hearing Detection and Intervention Programs. Joint Committee on Infant Hearing. 2019;4(2):1-44 see page 17 and 21]]

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